CGCT occurs in the mucosa of the maxillary alveolus as smooth surface pink mass, usually not associated with any other abnormality of the teeth or other congenital abnormalities [2
]. It have usually been sporadically presented as isolated case reports in British literature, since the first case was described in Germany in 1871 as a congenital epulis by Neumann [1
]. The tumor is postulated to originate from indifferentiatedmesenchymal cell, fibroblasts, myofibroblasts, histiocyts, Schwann cells or odontogenic epithelial cells; it is a benign mesenchymal tumor of unknown origin [4
]. CGCT is a very rare lesion that appears as a sessile or pedunculated lesions protruding from the neonate's mouth. The tumor occurs ten times more frequently in females than males and three times more frequently in the maxilla than mandible. It usually occurs as a single mass although 10% cases occur as multiple [5
]. They are usually less than 1,5cm diameter [6
]. Local excision is curative, with no reported recurrences in the literature, even when the excision has been incomplete [7
], the CGCT removal under local anesthesia is an alternative if intubation is not possible us in our case or in case of small lesion [8
]. Histopathology is the gold standard in the diagnostic process.