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BMJ Case Rep. 2010; 2010: bcr0820103280.
Published online Dec 6, 2010. doi:  10.1136/bcr.08.2010.3280
PMCID: PMC3028448
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A newborn with a genital prolapse
D M Borensztajn,1 K Haasnoot,1 G J Blok,1 and G M A Beckers2
1Department of Pediatrics, Medisch Centrum Alkmaar, Alkmaar, The Netherlands
2Department of Urology, VUMC Amsterdam, Amsterdam, The Netherlands
Correspondence to D M Borensztajn, dorineb/at/gmail.com
We describe a 3-week-old girl with a genital prolapse. She was seen postnatally because a prenatal ultrasound had shown a cystic dilation in the right kidney. Ultrasound showed two duplex kidneys, with hydronephrosis of the upper pole of the right kidney and a ureterocele in the bladder. Antibiotic prophylaxis was started while further investigations were awaited. At 3 weeks of age the patient presented to the emergency department with fever. Physical examination showed a moderately ill girl, with no obvious signs to explain the origin of the fever. Genital examination showed a blue cystic mass extruding from the vulva, most likely a ureterocele (figure 1). Urine culture was positive for Klebsiella oxytoca. Dimercaptosuccinic acid-scintigraphy showed an almost non-functioning upper pole of the right kidney. The patient was treated with intravenous antibiotics and made a good recovery. Voiding cystogram showed right-sided vesicoureteral reflux grade one to the lower pole.
Figure 1
Figure 1
Examination of the genitals of the girl showed a blue cystic mass extruding from the vulva. Ultrasound imaging confirmed the diagnosis of an ectopic ureterocele. A differential diagnosis of, for example, hymen imperforatus, can also be made by ultrasound. (more ...)
The girl was referred to a paediatric urologist for incision of the ureterocele. At the age of 12 months a resection of the right upper pole will be performed.
A ureterocele is a dilation of the distal ureter that is located within the bladder; if a portion is located at the bladder neck or urethra, it is termed ectopic or a cecoureterocele. Ureteroceles have an incidence of 1:500–1:4000.1 2 However, a ureterocele presenting as a vulval mass is rather rare and occurs in only 5–10% of all ureteroceles.1 3 When found, it is advisable to rule out other anomalies, such as duplex kidneys, since they frequently (80–90%) coincide.1 2
Footnotes
Competing interests None.
Patient consent Obtained.
References
1. Decter RM. Renal duplication and fusion anomalies. Pediatr Clin North Am 1997;44:1323–41. [PubMed]
2. Shokeir AA, Nijman RJ. Ureterocele: an ongoing challenge in infancy and childhood. BJU Int 2002;90:777–83. [PubMed]
3. Ilica AT, Kocaoglu M, Bulakbasi N, et al. Prolapsing ectopic ureterocele presenting as a vulval mass in a newborn girl. Diagn Interv Radiol 2008;14:33–4. [PubMed]
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