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Logo of annaldermaAnnals of DermatologyThis ArticleInformation for AuthorsOnline Submission
 
Ann Dermatol. Feb 2009; 21(1): 56–59.
Published online Feb 28, 2009. doi:  10.5021/ad.2009.21.1.56
PMCID: PMC2883371
A Case of Incontinentia Pigmenti Associated with Multiorgan Abnormalities
Woon-Kyong Chung, M.D., Deok-Woo Lee, M.D., Sung-Eun Chang, M.D., Mi-Woo Lee, M.D., Jee-Ho Choi, M.D., and Kee-Chan Moon, M.D.corresponding author
Department of Dermatology, University of Ulsan College of Medicine, Asan Medical Center, Seoul, Korea.
corresponding authorCorresponding author.
Reprint request to: Kee-Chan Moon, M.D., Department of Dermatology, University of Ulsan College of Medicine, Asan Medical Center, 388-1, Pungnap-dong, Songpa-gu, Seoul 138-736, Korea. Tel: 82-2-3010-3460, Fax: 82-2-486-7831, 1052_hihi/at/hanmail.net
Received April 18, 2008; Accepted August 5, 2008.
Abstract
Incontinentia pigmenti is a systemic disorder affecting the skin, teeth, eyes, nervous tissue, hair, nails, musculoskeletal system, and heart. We describe an 11-month-old girl with incontinentia pigmenti associated with a ventricular septal defect, left hemiatrophy, hemangiomas, an abnormal labial frenum, and spastic cerebral palsy manifested as left hemiplegia and developmental delay. We believe this patient illustrates that incontinentia pigmenti is a systemic disorder necessitating a multidisciplinary approach to management.
Keywords: Genodermatosis, Incontinentia pigmenti, Systemic disorder
Articles from Annals of Dermatology are provided here courtesy of
Korean Dermatological Association and Korean Society for Investigative Dermatology