(A) High resolution axial constructive interference in steady-state MR image of the inner ear and low brainstem of Patient 8 demonstrating normal inner ear structures and normal lower cranial nerves. (B, C) Axial CT (B) and T2-weighted MR images (C) at the level of the inner ear of Patient 6 demonstrating bilateral common cavity deformity (black arrow in B and white arrows in C). The medial part of the left carotid canal is absent (double arrows in B) while the right one is present. (D) Axial CT of the petrous bone of Patient 3 showing common cavity deformity of the left inner ear (open arrow) with normal stapes (double arrows) and lack of development of the oval window opposite to the footplate of stapes (solid arrow). (E) Reconstructed coronal CT image of the petrous bone of Patient 3 showing the common cavity deformity of the left inner ear (open arrow) and severe stenosis of the left internal auditory canal (black arrow). Inner ear structures on the right side are absent. (F) Coronal T2-weighted MR image of Patient 7 showing patulous Meckle's caves (arrows).