An 80‐year‐old man was seen with abnormal corneal appearances. He was asymptomatic with no previous ocular, medical or drug history. Visual acuities were 6/6 in both eyes unaided; with ocular examination revealing bilateral 0.1 mm wide white intrastromal corneal ring opacities 7.8 mm and 7.7 mm in diameter in the right and left eyes, respectively (fig 11).). Corneal sensation was normal with no evidence of thinning, scarring or vascularisation. The remaining ocular examination was normal. Blood tests for lipid, protein and autoimmune markers were normal. Corneal pachymetry and topography was unremarkable. Cross‐sectional imaging of the cornea with anterior segment optical coherence tomography (Visante OCT, Carl Zeiss Meditec, Inc., USA) revealed opacification affecting the entire thickness of the stroma (fig 22).). Confocal microscopy (HRT II/Rostock Cornea Module; Heidelberg Engineering GmbH, Germany) of the ring opacity revealed microdot extracellular deposits within the corneal stroma (fig 33).). The epithelium and endothelium of the cornea appeared normal. Ocular examination of the patient's sister was unremarkable, with another sister unavailable for examination. There has been no progression with over 12months follow‐up with the patient remaining asymptomatic.