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Heart. May 1998; 79(5): 513–515.
PMCID: PMC1728700
Truncus arteriosus with anterior origin of a hypoplastic main pulmonary artery
A Bensky and H Velvis
Department of Pediatrics, Bowman Gray School of Medicine of Wake Forest University, Winston-Salem, NC 27157, USA.
A newborn with an unusual form of truncus arteriosus is described, whose clinical presentation and certain features of her anatomy were more typical of pulmonary atresia with a ventricular septal defect. The morphological differentiation of certain types of truncus arteriosus and pulmonary atresia with ventricular septal defect remains an area of speculation among cardiac pathologists, and research in this area is being done using animal models. The anatomic features of the heart described in this report may assist in this discussion as the application of observations made in animal models to human cardiac development may be problematic.

Keywords: congenital heart disease;  truncus arteriosus;  echocardiography
Figure 1
Figure 1  
Short axis view of the quadricuspid truncal valve
Figure 2
Figure 2  
Parasternal long axis view showing the anterior origin of the main pulmonary artery (arrow).
Figure 3
Figure 3
Figure 3  
Selective angiogram showing the course of the main and left pulmonary artery. Figure 4   Truncal root angiogram showing the right aortic arch and the right pulmonary artery (arrow).
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