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J R Soc Med. 1987 January; 80(1): 17–20.
PMCID: PMC1290625

Retinitis pigmentosa and deafness.

Abstract

Seventeen patients with retinitis pigmentosa (RP) have been investigated audiologically. Of 9 found to have a significant hearing loss, 6 were examples of Usher's syndrome; these patients had a cochlear pattern of hearing loss. The other 3 were examples of Senior's syndrome, Kearne-Sayre syndrome and Lawrence-Moon-Biedle syndrome respectively. Two of these patients had absent stapedius reflexes. It is suggested that patients with different RP-deafness syndromes may have lesions in different parts of the auditory system.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.
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