PMCCPMCCPMCC

Search tips
Search criteria 

Advanced

 
Logo of archdischArchives of Disease in ChildhoodVisit this articleSubmit a manuscriptReceive email alertsContact usBMJ
 
Arch Dis Child. 1994 October; 71(4): 349–352.
PMCID: PMC1030018

Liver transplantation for hepatic cirrhosis in cystic fibrosis.

Abstract

Five children with cystic fibrosis complicated by hepatic cirrhosis received liver grafts. They all had portal hypertension with varices and three had variceal bleeding; respiratory function was only moderately impaired, but four were colonised with pseudomonas and one with aspergillus. Liver transplantation was well tolerated and there was no increase in respiratory or other early postoperative complications. Four of the children were fully well from 14 to 35 months after transplantation; the most recently transplanted had problems from a biliary stricture. In spite of the need for immunosuppression there was no increase in infection and respiratory function improved or remained stable. Once the children were stabilised after transplantation their nutrition and general health were greatly improved.

Full text

Full text is available as a scanned copy of the original print version. Get a printable copy (PDF file) of the complete article (665K), or click on a page image below to browse page by page.

Articles from Archives of Disease in Childhood are provided here courtesy of BMJ Group